Medley of Gynecological abnormalities around Hematocolpos

Abstract

A 12 year old girl not having attained menarche yet, presented with complaints of urinary retention and abdominal pain. Clinical examination and imaging confirmed the presence of hematocolpos secondary to both imperforate hymen and transverse vaginal septum. There was evidence of hydroureteronephrosis along with a septate uterus and vaginal agenesis (ESHRE Type U2b, C0, V4). Following Examination under Anesthesia, excision of the transverse vaginal septum was done along with drainage of menstrual blood and a vaginoplasty to correct the vaginal aplasia. This is a very rare and possibly one of the first reported cases of concurrent imperforate hymen, TVS, septate uterus and vaginal agenesis with hydroureteronephrosis.