MANAGEMENT OF MIDDLE AORTIC SYNDROME IN A 14-YEARS-OLD GIRL WITH TAKAYASU’S ARTERITIS

Authors

  • Fazaila Jabeen University of Child Health Sciences / The Children’s Hospital, Lahore, Pakistan
  • Samia Naz University of Child Health Sciences / The Children’s Hospital, Lahore, Pakistan
  • Shadab Masood University of Child Health Sciences / The Children's Hospital, Lahore
  • Sobia Qamar University of Child Health Sciences / The Children’s Hospital, Lahore, Pakistan
  • Rabbia Aman University of Child Health Sciences / The Children’s Hospital, Lahore, Pakistan
  • Masood Sadiq University of Child Health Sciences / The Children’s Hospital, Lahore, Pakistan

Abstract

A 14-years-old girl presented with pain in upper chest and left arm for 3 months associated with shortness of breath and headache. She had cold left upper limb with diminished pulses; and discrepancy of blood pressure in right upper limb as compared to left upper and both lower limbs. Echocardiography revealed left ventricular hypertrophy while CT-Angiography showed narrowing of descending thoracic aorta. She was diagnosed as Takayasu’s arteritis; and angiography revealed severe long-segment coarctation of descending thoracic aorta with obstruction of left common carotid and subclavian arteries. The coarctation of the aorta was successfully stented using a covered stent and patient was managed with steroids and methotrexate. At one-year follow-up; patient has improved symptoms, well-controlled hypertension and a patent stent on CT-angiography.

Published

2023-04-03

Issue

Vol. 47 No. 1 (2023)

Section

Case Report